Authors
PAOLA DI MAURO*, SALVATORE COCUZZA*, LUISA LICCIARDELLO*, LUIGI MAIOLINO*, GIACOMO SPINATO**, ALESSANDRO GULINO*, MILENA DI LUCA*, GIANLUCA CAMPIONE*, AGOSTINO SERRA*
Departments
* ENT Department - University of Catania, Italy -
**ENT Department - Rovigo Provincial Hospital, Italy
Abstract
The Charcot-Marie-Tooth (CMT) disease is a neurological syndrome, which has seldom been associated with hearing dysfunction, particularly sudden sensorineural hearing loss (SNHL). The disease of Charcot-Marie-Tooth is due to the alteration of one or more geniuses that give way to the formation of the assone and the genesis of the myelin, whose synthetic deficit involves the reduction of the speed of nervous management . The aim of the study was to detect in individuals suffering from Charcot-Marie-Tooth syndrome with audiological signs and symptoms qualitative and quantitative type of hearing impairment and of these finds some assumptions on the location of the damage along the auditory nerve pathways.
Keywords
Charcot-Marie-Tooth syndrome, hearing loss, otofunctional evaluation, sound distorsion.
DOI:
10.19193/0393-6384_2016_5_155
